EUROCJD

         European Creutzfeldt Jakob Disease Surveillance Network

 

 EUROCJD Surveillance Data

Total Cases of Sporadic CJD (Deaths)

 Sporadic CJD: Definite and probable cases

 Country 1993 1994 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 2006 2007 2008 2009 2010 Total
Australia 17 11 19 25 20 25 25 28 20 18 22 17 25 33 26 29 19 22 401
Austria 6 9 9 9 6 8 6 9 9 7 15 8 14 18 18 8 16 6 181
Belgium - - - - 10 15 13 9 16 22 20 20 12 15 16 4 10 12 194
Canada - 2 3 13 16 22 26 32 27 31 27 42 42 39 35 48 48 33 486
Cyprus - - 1 0 0 0 0 0 1 0 1 1 0 1 1 3 0 0* 9
Czech Republic - - - - - - - 2 8 6 8 11 10 10 11 11 15 13 105
Denmark - - - - 11 5 7 5 6 8 10 6 3 8 6 6 12 4 97
Estonia - - - - - - - - - - - 0 1 0 0 0 0 1 2
Finland - - - - 10 5 7 4 9 10 5 6 13 4 5 13 6 3* 100
France 35 45 59 68 80 81 92 88 109 107 108 97 83 124 138 105 114 145 1678
Germany 21 70 80 76 107 115 103 109 129 107 89 123 115 120 127 120 92 109 1812
Greece - - - - 6 4 7 9 8 11 6 7 5 6 7 6 n/a n/a 82
Hungary - - - - 11 3 5 9 17 7 8 8 8 12 13 14 7 14 136
Iceland - - - - 1 0 0 0 0 0 0 0 0 0 1 0 0 0 2
Ireland - - - 2 2 6 1 3 5 5 2 7 5 4 3 5 2 1* 50
Israel 2 1 3 3 4 5 3 3 4 3 8 8 6 5 5 8 7 1* 79
Italy 27 33 28 51 47 64 74 60 87 77 79 77 108 95 96 93 104 105 1305
Latvia - - - - - - - - - 0 0 0 0 0 1 1 0 2 4
Netherlands 12 18 8 14 18 17 19 10 14 18 12 20 20 22 15 16 11 29 293
Norway - - - - 6 2 2 3 5 2 6 7 4 5 5 4 5 1 57
Poland - - - - - - - - - 6 12 20 14 5 4 10 30 n/a 101
Portugal - - - - 5 6 5 5 16 6 11 6 10 5 8 4 6 2* 93
Slovakia 2 2 2 2 3 3 1 2 2 6 2 6 8 3 4 6 4 4 62
Slovenia 0 1 2 0 0 1 3 1 4 5 2 2 2 7 2 3 2 3 40
Spain 21 16 20 27 31 62 50 45 62 54 57 54 72 65 77 63 62 59 897
Sweden - - - - 10 14 11 14 12 12 11 15 13 16 11 13 11 13 176
Switzerland 8 10 10 10 10 8 9 11 19 18 17 16 10 13 16 14 18 5* 222
UK 36 54 35 40 60 64 62 50 58 72 79 50 67 69 64 88 78 84 1110

 

 

 Sporadic CJD: Annual mortality rates per million

  Country 1993 1994 1995 1996 1997 1998 1999 2000 2001 2002 2003 2004 2005 2006 2007 2008 2009 2010 Mean Rate
Australia 0.96 0.62 1.05 1.37 1.08 1.34 1.32 1.46 1.03 0.92 1.11 0.84 1.23 1.59 1.23 1.35 0.87 0.98 1.13
Austria 0.77 1.15 1.15 1.15 0.77 1.03 0.77 1.12 1.12 0.87 1.86 0.99 1.74 2.23 2.23 0.99 1.98 0.75 1.25
Belgium - - - - 0.97 1.46 1.26 0.87 1.55 2.14 1.94 1.94 1.17 1.46 1.55 0.37 0.93 1.13 1.34
Canada 0.07 0.1 0.44 0.53 0.73 0.86 1.04 0.87 0.99 0.85 1.31 1.3 1.2 0.06 1.44 1.42 0.98 1.11
Cyprus - - 1.48 0 0 0 0 0 1.43 0 1.39 1.37 0 1.30 1.28 3.84 0 0* 0.78
Czech Republic - - - - - - - 0.19 0.78 0.59 0.78 1.08 0.98 0.97 1.07 1.05 1.43 1.23 0.92
Denmark - - - - 2.08 0.94 1.32 0.94 1.12 1.51 1.89 1.13 0.57 1.51 1.1 1.09 2.18 0.73 1.29
Estonia - - - - - - - - - - - 0 1.35 0 0 0 0 0.75 0.21
Finland - - - - 1.92 0.96 1.35 0.77 1.73 1.92 0.96 1.15 2.5 0.77 0.72 2.5 1.13 0.28* 1.41
France 0.6 0.8 1.02 1.18 1.38 1.38 1.53 1.46 1.79 1.76 1.76 1.56 1.3 1.97 2.17 1.63 1.78 2.25 1.52
Germany 0.44 0.85 1 0.93 1.3 1.4 1.25 1.36 1.6 1.3 1.1 1.5 1.4 1.5 1.5 1.5 1.1 1.3 1.24
Greece - - - - 0.55 0.37 0.64 0.83 0.73 1 0.55 0.64 0.46 0.55 0.63 0.54 n/a n/a 0.62
Hungary - - - - 1.1 0.3 0.5 0.9 1.7 0.7 0.8 0.8 0.8 1.2 1.3 1.4 0.7 1.4 0.97
Iceland - - - - 3.7 0 0 0 0 0 0 0 0 0 3.23 0 0 0 0.53
Ireland - - - 0.55 0.55 1.62 0.27 0.79 1.3 1.28 0.5 1.73 1.21 0.94 0.71 1.18 0.47 0.24* 0.92
Israel 0.37 0.19 0.56 0.49 0.66 0.82 0.49 0.49 0.6 0.45 1.2 1.2 0.9 0.68 0.68 1.1 0.82 0.13* 0.69
Italy 0.48 0.58 0.49 0.89 0.83 1.11 1.35 1.04 1.5 1.35 1.37 1.35 1.87 1.64 1.66 1.61 1.8 1.81 1.25
Latvia - - - - - - - - - 0 0 0 0 0 0.43 0.43 0 0.89* 0.22
Netherlands 0.79 1.17 0.52 0.9 1.2 1.13 1.24 0.63 0.88 1.13 0.75 1.22 1.22 1.34 0.92 0.98 0.66 1.74 1.02
Norway - - - - 1.33 0.44 0.44 0.67 1.11 0.44 1.33 1.56 0.89 1.08 1.11 0.86 1.04 0.2 0.95
Poland - - - - - - - - - 0.16 0.31 0.52 0.36 0.13 0.08 0.26 0.86 n/a 0.34
Portugal - - - - 0.5 0.6 0.5 0.5 1.6 0.6 1.1 0.6 1 0.5 0.8 0.4 0.56 0.19* 0.7
Slovakia 0.4 0.4 0.4 0.4 0.6 0.6 0.2 0.4 0.4 1.13 0.4 1.17 1.34 0.57 0.75 1.13 0.74 0.74 0.65
Slovenia 0 0.5 1 0 0 0.5 1.51 0.5 2.01 2.51 1 1 1 3.49 0.99 1.46 0.99 0.5 1.12
Spain 0.54 0.41 0.51 0.69 0.79 1.57 1.27 1.14 1.57 1.36 1.44 1.36 1.81 1.49 1.74 1.39 1.37 1.28 1.22
Sweden - - - - 1.13 1.58 1.24 1.58 1.35 1.34 1.23 1.66 1.44 1.76 1.2 1.4 1.18 1.39 1.39
Switzerland 1.15 1.42 1.42 1.41 1.41 1.12 1.26 1.53 2.62 2.46 2.31 2.16 1.34 1.73 2.11 1.81 2.4 1.04* 1.7
UK 0.62 0.93 0.6 0.69 1.03 1.09 1.06 0.85 0.98 1.21 1.33 0.84 1.11 1.14 1.05 1.43 1.26 1.35 1.024

 *to 30 June 2010              n/a = not available   

 

Total Cases of CJD/GSS (Deaths)

vCJD cases Worldwide

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